Amniotic bands sequence is a congenital disorder characterized by craniofacial, body wall, and limb anomalies that may be associated with fetalplacental fibrous bands. Its prevalence has been reported to range from 0. Different theories have attempted to explain the etiology of amniotic band sequence; however, none has individually been able to support each and every defect observed, so it has been considered to be a multifactorial condition. The pre- and post-natal identification of anomalies suggestive of amniotic band sequence is useful for the diagnostic approach and implementation of timely therapeutic interventions favoring the release of the amniotic bands using fetoscopy with recovery of the involved distal limb perfusion, or else the possibility of performing a post-natal surgical repair. It is also helpful to provide genetic counseling.
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Publication date Print : December Introduction: amniotic band syndrome includes a group of sporadic congenital anomalies characterized by fibrous rings that cause severe external and internal structural fetal defects. The most frequent defects are those affecting the fetus's limps- digits, arms and legs- may lead to amputations. Objective: to highlight the importance of early diagnosis of congenital malformations by ultrasonography in primary health care.
Methods: ultrasonographic images of a case of prenatal diagnosis of amniotic band syndrome at 18 weeks of gestation are presented here. This syndrome produced serious fetal extremities and face alterations in a case, with no other ultrasonographic findings. Results: prior genetic counseling, the couple decided the termination of pregnancy. Conclusion: the case was confirmed by pathology as an amniotic band syndrome with structural fetal defects. Data availability:.
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An Update on Amniotic Bands Sequence
Rev Mex Pediatr ; Amniotic band syndrome: 3 case reports. Rev Chil Pediatr ; Amniotic band syndrome congenital anular constrictions. European Acad Dermatol and Venereol ; Arch Argent Pediatr ;
2005, Número 2
ISSN The amniotic band syndrome ABS is characterized by accumulation of fibrous tissue bands or strings that adhere to the fetus and may produce compression in different sites. Most cases present multiple congenital anomalies incompatible with life. A small group of fetuses have isolated constrictions of the limb that may cause severe limb dysfunction or limb amputation if not treated during pregnancy. This rare condition occurs in approximately to live births. The exact cause of ABS remains uncertain; however, theories of intrinsic, extrinsic and iatrogenic reasons have been proposed. The evolution of the limb affected by ABS is characterized by progression of distal edema due to venous obstruction, and intrauterine amputation of the limb from vascular insufficiency.